A 51-year-old woman with polycystic liver and kidney disease had undergone renal transplantation 21 years before presentation. She had no evidence of cerebrovascular malformations. Both her father and aunt also had polycystic kidney disease. After the renal transplantation, her liver had become progressively diseased and enlarged through cystic changes. Early satiety, malnutrition, and abdominal pain necessitated a liver transplantation. A 9.1-kg liver (white arrow) was removed and replaced with a whole graft that was one tenth the weight of the diseased liver (black arrowhead). A large cyst at the dome of the native liver had to be decompressed (white arrowhead) to allow for access to the recipient's suprahepatic vena cava. She made an excellent recovery and had normal kidney and liver function at 4 years of follow-up.
I have seen numerous PCOS and kidney's that look like this, bit this has got to be the largest diseased livers I have ever seen. Bless her heart!! I bet she felt so much better!