Ulnar dimelia is a rare developmental anomaly, which is characterized by absence of radius, duplication of ulna and symmetric polydactyly (seven or eight fingers and lack of thumb). Ulnar dimelia is a very rare developmental anomaly of the upper limb. There are only approximately 70 cases described in the literature. Ulnar dimelia, called also the mirror-hand, is classified to the 3rd group of congenital hand malformation, according to the classification proposed by Swanson and adopted by the American Society for Surgery of the Hand (ASSH) and the International Federation of Societies for Surgery of the Hand (IFSSH). Skeletal malformation may be followed by arterial and nervous anomalies as an absence of the radial artery, duplication of the ulnar artery, presence of abnormal arterial arches in the hand, shortening of radial nerve, duplication of ulnar nerve (sometimes with collaterals to median nerve). Tag a friend and follow us at @Medicalpedia