Dr Obaid Alademiover 6 years ago

15 years old child presents to my clinic c/o inability to walk or rise from floor since 2 month back. The condition started 3month back by regurgitation of fluid from nose which is treated by ENT Doctor with out any document. On exam cranial nerves are intact, intact bulk of muscles, generalized hypotonia in both Uls & LLs. Arflxia also. Up going bilateral planter response. Intact both sup. & deep sensation. With ataxic gait and gower sign is positive. No past history of infection preceded neither drug intake. Family history irrelevant What's are your DDx?